TI : A case of cleidocranial dysostosis
AU : Lim CY*; Kim SW*; Ahn HK; You DS; Park TW
AD : *Department of Oral Pathology, Department of Dental Roentgenology, College of Dentistry, Seoul National University
SO : JKAMFR. 1977;7(1):49-52
PY : 1977
LA : KOREAN
CP : KOREA
AB : The authors had observed a case of cleidocranial dysostosis of 42 year old unmarried woman.
The observation was founded upon roentgenogram of skull P-A view, orthopantomograph, cephalometric view, chest P-A view , and wrist X-ray view.
The patient gave a dwarfish impression with 145 cm body height and concave mandibular prognathic facial feature. The palate was narrowed and extremely high arched.
The eruption state of teeth was extremely poor, only four teeth were erupted, composed of upper third molar and lower three deformed teeth.
The skull P-A view of reontgenogram reveals overlying metopic suture, and the suture are delayed up to date and many wormian bones are formed. On the cephalometric view, the maxilla is underdeveloped and produce the false mandibular prognathism.
Twenty four impacted teeth can be detected by orthopantmograph, twelve in upper jaw and twelve in lower jaw. There are many supernumerary teeth, one in upper jaw and seven in lower jaw.
On the chest P-A view, the clavicles are totally aplastic, but a vestige of clavicle is visible in the right side. On the wrist roentgenogram, the epiphyseal ossification of distal phalanx, mesial phalanx, and proximal phalanx is delayed.